Successful treatment of a patient aged 1 month with long QT syndrome and multiple episodes of ventricular fibrillation

  • S. Yu. Prorok State Institution “Scientific and Practical Centre for Pediatric Cardiology and Cardiac Surgery of the MoH of Ukraine” (Kyiv)
  • O. S. Proidak State Institution “Scientific and Practical Centre for Pediatric Cardiology and Cardiac Surgery of the MoH of Ukraine” (Kyiv)
  • M. S. Meshkova State Institution “Scientific and Practical Centre for Pediatric Cardiology and Cardiac Surgery of the MoH of Ukraine” (Kyiv)
  • O. V. Doronin P. L. Shupyk National Academy of Postgraduate Education (Kyiv)
  • N. M. Rudenko P. L. Shupyk National Academy of Postgraduate Education (Kyiv)
Keywords: long QT syndrome, pacing, β-blockers

Abstract

Long QT syndrome (LQTS) is a rare condition associated with sudden cardiac death. Accumulation of experience of the successful management of patients under the age of 1 year old with LQTS is a relevant issue.

Objective. To analyse the com-plex case of treatment of a patient with LQTS.

Materials and methods. Treatment of a symptomatic patient aged 1 month with LQTS was performed.

Results and discussion. We have a successful experience of epicardial pacing in combination with β-blockers.

Conclusion. Prescription of β-blocker maximal doses and epicardial pacing is the efficient treatment method in patients under 1 year of age with LQTS and unstable hemodynamics.

References

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4. The Jervell and Lange-Nielsen syndrome; atrial pacing combined with Я-blocker therapy, a favorable approach in young high-risk patients with long QT syndrome? / Frьh A., Siem G., Holmstrцm H. et al. // Heart Rhythm. – 2016 Nov. – Vol. 13 (11). – P. 2186–2192. doi: 10.1016/j. hrthm.2016.07.020. Epub 2016 Jul 20.

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Published
2018-09-17
How to Cite
Prorok, S. Y., Proidak, O. S., Meshkova, M. S., Doronin, O. V., & Rudenko, N. M. (2018). Successful treatment of a patient aged 1 month with long QT syndrome and multiple episodes of ventricular fibrillation. Ukrainian Journal of Cardiovascular Surgery, (3 (32), 77-79. https://doi.org/10.30702/ujcvs/18.32/19(077-079)