The outcomes of the extracardiac total cavopulmonary connection in 130 consecutive patients with single-ventricle physiology

  • E. M. Bairamov Ukrainian Children’s Cardiac Center, Kiev, Ukraine
  • Y. V. Poznyak Ukrainian Children’s Cardiac Center, Kiev, Ukraine
  • O. M. Dovgan Shupyk National Medical Academy of Postgraduate Education
  • N. M. Rudenko Shupyk National Medical Academy of Postgraduate Education
  • I. M. Yemets Ukrainian Children’s Cardiac Center, Kiev, Ukraine
Keywords: single ventricle, extracardiac total cavopulmonary connection, extracardiac conduit

Abstract

Fontan procedure has gone through several modifications and today is the primary palliation to treat a broad spectrum of com-plex congenital heart defects.

The aim of this study is to present the results of treatment of children and adults with a single ventricle.

Materials and methods. Since 2005 to 2015 years, in 130 consecutive patients with a single ventricle morphology aged 9,97±4,37 years the extracardiac total cavopulmonary connection was performed. The most common heart pathology was tricus-pid atresia (26,9%). In 118 (90,8%) patients, the operation was carried out with the moderately hypothermic cardiopulmonary bypass, without aortic cross-clamp. The average cardiopulmonary bypass time was 94,2±56,6 min. In the remaining twelve patients extracardiac TCPC was carried out without CPB.

Results. There were three (2,3%) early deaths. The median duration of the mechanical ventilation was 9,7±16,1 h (1–71 h). The average length of stay was 17,5±18,5 days (8,0–81,0 days).

Conclusions. Improved understanding of single-ventricle physiology, patient preparation, surgical techniques, and post-operative care has allowed us to reach a steady state in the early outcomes after TCPC.

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Published
2017-05-15
How to Cite
Bairamov, E. M., Poznyak, Y. V., Dovgan, O. M., Rudenko, N. M., & Yemets, I. M. (2017). The outcomes of the extracardiac total cavopulmonary connection in 130 consecutive patients with single-ventricle physiology. Ukrainian Journal of Cardiovascular Surgery, (1 (27), 78-83. Retrieved from http://cvs.org.ua/index.php/ujcvs/article/view/183
Section
CONGENITAL HEART DEFECTS