The first experience of pulmonary valve perforation with concomitant arterial duct stenting in patients with pulmonary atresia and intact interventricular septum

  • A. V. Maksymenko Ukrainian Children’s Cardiac Center (Kyiv)
  • Y. L. Kuzmenko Ukrainian Children’s Cardiac Center (Kyiv)
  • A. A. Dovhaliuk Ukrainian Children’s Cardiac Center (Kyiv)
  • O. O. Motrechko Ukrainian Children’s Cardiac Center (Kyiv)
  • O. R. Vitovska Ukrainian Children’s Cardiac Center (Kyiv)
Keywords: pulmonary atresia, pulmonary valve perforation, arterial duct stenting

Abstract

Pulmonary atresia with intact interventricular septum (PAIVS) – is a complex congenital heart disease characterized by a valve atresia with attendant right ventricle (RV) and a tricuspid valve (TV) hypoplasia of varying degrees with duct-dependent pulmonary circulation. One of the modern methods of treating PAIVS is pulmonary valve perforation with subsequent arterial duct stenting.

Purpose – to present first experience of the PV perforation with concomitant arterial duct stenting in patients with PAIVS.

Materials and methods. Three neonates with PAIVS were performed concomitant PV perforation with arterial duct stenting in UCCC.

Results and discussion. The procedure was successful in three newborn patients with moderate RV hypoplasia with a membranous PV atresia with IVS. On average, after intervention, patients were in the ICU for 5 days, two of them needed ventilatory support, one – sympathomimetic support. The median length of hospital stay was 13 days. Postoperative compli-cations were not observed. There was no early mortality.

Conclusions. PV perforation with concomitant arterial duct stenting is an effective and safe method for optimizing pul-monary circulation in patients with PAIVS with moderate RV hypoplasia.

References

1. Alwi M. Management algorithm in pulmonary atresia with intact ventricular septum // Catheter Cardiovasc Interv. – 2006. – Vol. 67. – P. 679–86.

2. Comparison of Ductal Stenting Versus Surgical Shunts for Palliation of Patients With Pulmonary Atresia and Intact Ventricular Septum / Kiran Mallula, Gabrielle Vaughn, Howaida El-Said et al. // Catheter CardiovascInterv. – 2015. – Vol. 85 (7). – P. 1196–202. doi: https://doi.org/10.1002/ccd.25870.

3. Duct Stenting Versus Modified Blalock-Taussig Shunt in Neonates With Duct-Dependent Pulmonary Blood Flow: Associations With Clinical Outcomes in a Multicenter National Study / James R. Bentham, Ngoni K. Zava, Wendy J. Harrison et al. //Circulation. – 2018. – Vol. 137. – P. 581– 588. doi: https://doi.org/10.1161/CIRCULATIONAHA.117.028972.

4. Ductus Arteriosus Patency With Stenting in CriticalPulmonary Stenosis and Pulmonary AtresiaWith Intact Interventricular Septum / Carlos Mortera, Miquel Rissech, Joaquim Bartrons et al. // Rev EspCardiol. – 2005. – Vol. 58 (5). – P. 592–5.

5. More Than 25 Years of Experience in ManagingPulmonary Atresia With Intact Ventricular Septum / Adriaan W. Schneider, Nico A. Blom, Eline F. Bruggemans et al. // Ann ThoracSurg. – 2014. – Vol. 98. – P. 1680–6.

6. Transcatheter pulmonary valve perforation using chronic total occlusion wire in pulmonary atresia with intact ventricular septum / Shweta Bakhru, Shilpa Marathe, Manish Saxena et al. // Annals of Pediatric Cardiology. – 2017. – Vol. 10 (1). – P. 5–10.
Published
2018-03-12
How to Cite
Maksymenko, A. V., Kuzmenko, Y. L., Dovhaliuk, A. A., Motrechko, O. O., & Vitovska, O. R. (2018). The first experience of pulmonary valve perforation with concomitant arterial duct stenting in patients with pulmonary atresia and intact interventricular septum. Ukrainian Journal of Cardiovascular Surgery, (1 (30), 85-89. https://doi.org/10.30702/ujcvs/18.30/18(085-089)